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718096004: Hepatoportal sclerosis (disorder)


Status: current. Date: 31-Jul 2016

Descriptions:

Id Description Lang Type Status Case? Module
3311104019 Hepatoportal sclerosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3311147019 Hepatoportal sclerosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3311148012 Obliterative portal venopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3311149016 A rare disorder with characteristics of sclerosis of the intrahepatic portal veins, non-cirrhotic portal hypertension, asymptomatic splenomegaly and recurrent variceal bleeding. Most commonly, the condition is detected in investigating a fortuitous finding of hypersplenism or splenomegaly. Main histopathologic findings are periportal fibrosis, occlusion of small portal veins, sclerosis of the portal venous system, and proliferation of small vascular channels within/around portal tracts. The disease is slowly progressive. Exposure to toxic substances or drugs, autoimmune and connective tissue diseases, systemic or intraabdominal infections, and clotting abnormalities have been incriminated. A genetic background has been suggested. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core
5401664014 A form of porto-sinusoidal vascular disease characterized histologically by varying degrees of phlebosclerosis, primarily involving the small and medium branches of the portal vein with heterogeneous distribution, in the absence of cirrhosis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5401665010 A form of porto-sinusoidal vascular disease characterised histologically by varying degrees of phlebosclerosis, primarily involving the small and medium branches of the portal vein with heterogeneous distribution, in the absence of cirrhosis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Hepatoportal sclerosis (disorder) Is a Porto sinusoidal vascular disease (disorder) true Congenital syphilitic hepatomegaly Congenital syphilitic hepatomegaly
Hepatoportal sclerosis (disorder) Associated morphology Vascular sclerosis true Congenital syphilitic hepatomegaly Congenital syphilitic hepatomegaly 1
Hepatoportal sclerosis (disorder) Finding site Structure of intrahepatic part of main portal vein (body structure) true Congenital syphilitic hepatomegaly Congenital syphilitic hepatomegaly 1
Hepatoportal sclerosis (disorder) Finding site Vascular structure of liver true Congenital syphilitic hepatomegaly Congenital syphilitic hepatomegaly 2

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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