715401008: Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)

SNOMED CT Concept\Clinical finding (finding)\...

\Hypersensitivity condition\Cell-mediated cytotoxic disorder (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)

\Viscus structure finding (finding)\Liver finding\Disease of liver\...

\Structural abnormality of liver (disorder)\Lesion of liver\Hepatic fibrosis\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Cholangiohepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Structural abnormality of liver (disorder)\Liver regeneration\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)

\Chronic liver disease\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)

\Autoimmune liver disease\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)

\Finding of trunk structure\Liver finding\Disease of liver\Structural abnormality of liver (disorder)\Lesion of liver\Hepatic fibrosis\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Liver finding\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Liver finding\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Cholangiohepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Liver finding\Disease of liver\Structural abnormality of liver (disorder)\Liver regeneration\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Liver finding\Disease of liver\Chronic liver disease\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Liver finding\Disease of liver\Autoimmune liver disease\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Lesion of liver\Hepatic fibrosis\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Cholangiohepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Liver regeneration\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disease of liver\Chronic liver disease\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disease of liver\Autoimmune liver disease\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)

\Disease\Cell-mediated cytotoxic disorder (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of body system\Disease of liver\Structural abnormality of liver (disorder)\Lesion of liver\Hepatic fibrosis\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of body system\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of body system\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Cholangiohepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of body system\Disease of liver\Structural abnormality of liver (disorder)\Liver regeneration\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of body system\Disease of liver\Chronic liver disease\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of body system\Disease of liver\Autoimmune liver disease\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Scleroderma\Systemic sclerosis with limited cutaneous involvement\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Lesion of liver\Hepatic fibrosis\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Inflammatory disease of liver\Cholangiohepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of trunk (disorder)\Disease of liver\Structural abnormality of liver (disorder)\Liver regeneration\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of trunk (disorder)\Disease of liver\Chronic liver disease\Cirrhosis of liver\Biliary cirrhosis\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Disorder of trunk (disorder)\Disease of liver\Autoimmune liver disease\Autoimmune hepatitis (disorder)\Primary biliary cholangitis\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)
\Disease\Systemic disease\Systemic sclerosis with limited cutaneous involvement\Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)

Status: current. Date: 31-Jul 2019

Descriptions:

Id Description Lang Type Status Case? Module

3302234010 Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3302235011 Primary biliary cirrhosis co-occurrent with systemic scleroderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3302236012 Reynolds syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3302474019 An autoimmune disorder characterized by the association of primary biliary cirrhosis with limited cutaneous systemic sclerosis. Onset occurs between 30-65 years. Occurs sporadically, but rare familial cases with an unknown inheritance pattern have been observed. There is no cure and management is mainly supportive. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core
3302475018 An autoimmune disorder characterised by the association of primary biliary cirrhosis with limited cutaneous systemic sclerosis. Onset occurs between 30-65 years. Occurs sporadically, but rare familial cases with an unknown inheritance pattern have been observed. There is no cure and management is mainly supportive. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core
5400852010 Reynolds syndrome (RS) is an autoimmune disorder characterized by the association of primary biliary cirrhosis (PBC) with limited cutaneous systemic sclerosis (lcSSc). en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5400853017 Reynolds syndrome (RS) is an autoimmune disorder characterised by the association of primary biliary cirrhosis (PBC) with limited cutaneous systemic sclerosis (lcSSc). en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Is a	Systemic sclerosis with limited cutaneous involvement	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Is a	Primary biliary cholangitis	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Associated morphology	Fibrosis	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	1
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Finding site	Connective tissue structure	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	1
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Pathological process (attribute)	Autoimmune process	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	1
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Associated morphology	Inflammatory morphology (morphologic abnormality)	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	2
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Finding site	Structure of intrahepatic bile duct (body structure)	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	2
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Pathological process (attribute)	Autoimmune process	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	2
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Associated morphology	Chronic fibrosis	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	3
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Finding site	Structure of intrahepatic bile duct (body structure)	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	3
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Pathological process (attribute)	Autoimmune process	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	3
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Associated morphology	Nodular regeneration	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	4
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Finding site	Structure of intrahepatic bile duct (body structure)	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	4
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Pathological process (attribute)	Autoimmune process	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	4
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Clinical course	Progressive	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	5
Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	Pathological process (attribute)	Hypersensitivity process (qualifier value)	true	Congenital syphilitic hepatomegaly	Congenital syphilitic hepatomegaly	6

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

This concept is not in any reference sets

Back to Start

Id	Description	Lang	Type	Status	Case?	Module
3302234010	Primary biliary cirrhosis co-occurrent with systemic scleroderma (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3302235011	Primary biliary cirrhosis co-occurrent with systemic scleroderma	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3302236012	Reynolds syndrome	en	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
3302474019	An autoimmune disorder characterized by the association of primary biliary cirrhosis with limited cutaneous systemic sclerosis. Onset occurs between 30-65 years. Occurs sporadically, but rare familial cases with an unknown inheritance pattern have been observed. There is no cure and management is mainly supportive.	en	Definition	Inactive	Entire term case sensitive (core metadata concept)	SNOMED CT core
3302475018	An autoimmune disorder characterised by the association of primary biliary cirrhosis with limited cutaneous systemic sclerosis. Onset occurs between 30-65 years. Occurs sporadically, but rare familial cases with an unknown inheritance pattern have been observed. There is no cure and management is mainly supportive.	en	Definition	Inactive	Entire term case sensitive (core metadata concept)	SNOMED CT core
5400852010	Reynolds syndrome (RS) is an autoimmune disorder characterized by the association of primary biliary cirrhosis (PBC) with limited cutaneous systemic sclerosis (lcSSc).	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
5400853017	Reynolds syndrome (RS) is an autoimmune disorder characterised by the association of primary biliary cirrhosis (PBC) with limited cutaneous systemic sclerosis (lcSSc).	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core