Status: current. Date: 01-May 2025
Descriptions:
| Id | Description | Lang | Type | Status | Case? | Module |
| 5455788018 | PSVD - porto sinusoidal vascular disease | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| 5455789014 | Porto sinusoidal vascular disease (disorder) | en | Fully specified name | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
| 5455790017 | Portosinusoidal vascular disease | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
| 5455793015 | Porto sinusoidal vascular disease | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
| 5455794014 | Porto-sinusoidal vascular disease | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
| 5455795010 | A rare vascular liver disease characterised by the absence of cirrhosis with or without portal hypertension and histological lesions involving portal venules or sinusoids. Patients may present either with specific clinical signs of portal hypertension (including gastric oesophageal or ectopic varices, portal hypertensive bleeding or porto-systemic collaterals at imaging) or a histological lesion specific to porto sinusoidal vascular disease (including obliterative portal venopathy, nodular regenerative hyperplasmia or incomplete septal fibrosis or cirrhosis) or they may manifest clinical signs that are not specific to portal hypertension (such as ascites, platelet count <150.000/µl, increased spleen size ≥13 cm in the largest axis) together with a histological lesion including portal tract abnormalities, irregular distribution of the portal tracts and central veins, non-zonal sinusoidal dilation, mild perisinusoidal fibrosis. Possible associations with altered immunity, haematological diseases and prothrombotic conditions, infections, congenital or familial defects, or drug exposure are reported. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| 5455796011 | A rare vascular liver disease characterized by the absence of cirrhosis with or without portal hypertension and histological lesions involving portal venules or sinusoids. Patients may present either with specific clinical signs of portal hypertension (including gastric esophageal or ectopic varices, portal hypertensive bleeding or porto-systemic collaterals at imaging) or a histological lesion specific to porto sinusoidal vascular disease (including obliterative portal venopathy, nodular regenerative hyperplasmia or incomplete septal fibrosis or cirrhosis) or they may manifest clinical signs that are not specific to portal hypertension (such as ascites, platelet count <150.000/µl, increased spleen size ≥13 cm in the largest axis) together with a histological lesion including portal tract abnormalities, irregular distribution of the portal tracts and central veins, non-zonal sinusoidal dilation, mild perisinusoidal fibrosis. Possible associations with altered immunity, hematological diseases and prothrombotic conditions, infections, congenital or familial defects, or drug exposure are reported. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
| Porto sinusoidal vascular disease (disorder) | Is a | Vascular disorder of liver | true | Congenital syphilitic hepatomegaly | Congenital syphilitic hepatomegaly | ||
| Porto sinusoidal vascular disease (disorder) | Finding site | Vascular structure of liver | true | Congenital syphilitic hepatomegaly | Congenital syphilitic hepatomegaly | 1 |
| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
| Hepatoportal sclerosis (disorder) | Is a | True | Porto sinusoidal vascular disease (disorder) | Congenital syphilitic hepatomegaly | Congenital syphilitic hepatomegaly |
This concept is not in any reference sets
FHIR