Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 01-Jul 2024. Module: IPS terminology module (core metadata concept)
Descriptions:
| Id | Description | Lang | Type | Status | Case? | Module |
| 3687582015 | Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | en | Fully specified name | Active | Entire term case sensitive (core metadata concept) | IPS terminology module (core metadata concept) |
| 3687583013 | Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | IPS terminology module (core metadata concept) |
| 3687587014 | Toxic epidermolysis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | IPS terminology module (core metadata concept) |
| 3687603019 | An acute and severe skin disease with clinical and histological features of destruction and detachment of the skin epithelium and mucous membranes. Onset may occur at any age, but the risk increases after 40 years. Three subforms have been described according to the percentage of the body surface area affected: Stevens-Johnson syndrome (less than 10%), Lyell syndrome (greater than 30%) and an intermediate form (10-29%). The initial manifestations are nonspecific: a seemingly banal rash, fever, and a burning sensation involving the eyes, mouth and genitalia. The rash rapidly progresses to become vesicular and bullous on the face and body. High fever is a constant feature. Two thirds of cases are triggered by a drug allergy. In rare cases, the disease is associated with infections or bone marrow transplantation. The remaining 25-30% of cases are classed as idiopathic. The prognosis for patients with extensive forms is poor. | en | Definition | Active | Entire term case sensitive (core metadata concept) | IPS terminology module (core metadata concept) |
| Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Is a | Erythema | true | Inferred relationship | Some | ||
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Is a | Acute disease | true | Inferred relationship | Some | ||
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Is a | Eruption | true | Inferred relationship | Some | ||
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Is a | Skin necrosis | true | Inferred relationship | Some | ||
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Associated morphology | Eruption | true | Inferred relationship | Some | 1 | |
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Finding site | Skin structure | true | Inferred relationship | Some | 1 | |
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Associated morphology | Necrosis | true | Inferred relationship | Some | 2 | |
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Finding site | Skin structure | true | Inferred relationship | Some | 2 | |
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Associated morphology | Erythema | true | Inferred relationship | Some | 3 | |
| Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Clinical course | Sudden onset AND/OR short duration (qualifier value) | true | Inferred relationship | Some | 4 |
| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
| Stevens-Johnson syndrome | Is a | True | Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Inferred relationship | Some | |
| Lyell syndrome (disorder) | Is a | True | Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | Inferred relationship | Some |
Reference Sets
FHIR