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773986009: Nevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3727473019 Nevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3727474013 NEVADA (nevus epidermicus verrucosus with angiodysplasia and aneurysm) syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3727475014 NEVADA (naevus epidermicus verrucosus with angiodysplasia and aneurysm) syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3727476010 NEVADA syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3727478011 Nevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3727479015 Naevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3727472012 A rare life-threatening cutaneous disease characterized by a keratinocytic epidermal nevus presenting thick, hystrix-like, white or brownish hyperkeratosis associated with multiple extracutaneous vascular malformations, including angiodysplasia that involves large-vessel arteriovenous shunts that may be fatal during the neonatal period. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3727477018 A rare life-threatening cutaneous disease characterised by a keratinocytic epidermal naevus presenting thick, hystrix-like, white or brownish hyperkeratosis associated with multiple extracutaneous vascular malformations, including angiodysplasia that involves large-vessel arteriovenous shunts that may be fatal during the neonatal period. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Nevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome (disorder) Finding site Skin structure true Inferred relationship Some 1
Nevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome (disorder) Associated morphology Epidermal nevus true Inferred relationship Some 1
Nevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome (disorder) Is a Verrucous epidermal nevus (disorder) true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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