Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2017. Module: SNOMED CT core
Descriptions:
| Id | Description | Lang | Type | Status | Case? | Module |
| 3324678017 | A life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease, with the association of multiple pulmonary artery aneurysms and peripheral venous thrombosis. Prevalence is unknown but fewer than 30 cases have been reported in the literature since its first description in 1959 by Hughes and Stovin. Patients (mostly men aged 12-40 years) generally present with the nonspecific signs of pulmonary artery aneurysms, following a history of peripheral venous thrombosis. Other associated signs may include fever and intracranial hypertension. Aneurysms can occur anywhere in the systemic circulation. Recurrent phlebitis also commonly involves the large vessels, resulting in thrombus formation. In general, there is a predisposition for thrombus formation affecting the peripheral veins. It is assumed the disease is a form of vasculitis following a similar mechanism of pathogenesis to that thought to be involved in Behcet disease. | en | Definition | Inactive | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| 5402650011 | Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| 5402651010 | Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterised by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| 3324673014 | Hughes Stovin syndrome (disorder) | en | Fully specified name | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| 3324676018 | Hughes Stovin syndrome | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
| Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. | Associated morphology | Inflammation | false | Inferred relationship | Some | 1 | |
| Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. | Finding site | Systemic vascular structure | true | Inferred relationship | Some | 1 | |
| Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. | Is a | Vasculitis | false | Inferred relationship | Some | ||
| Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. | Associated morphology | Inflammatory morphology (morphologic abnormality) | true | Inferred relationship | Some | 1 | |
| Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. | Is a | Inflammation of systemic vasculature (disorder) | true | Inferred relationship | Some |
| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
Reference Sets
Component annotation with string value reference set (foundation metadata concept)
FHIR