717191005: Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)

Id Description Lang Type Status Case? Module

3308645013 Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3308646014 Sporadic idiopathic steroid-resistant nephrotic syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3308647017 Sporadic idiopathic nephrosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3308648010 A heterogeneous entity. Its prevalence in the general population is unknown. Nephrotic syndrome has manifestations of marked proteinuria, with reduced plasmatic levels of albumin, and potentially with oedema. Familial forms are in most cases related to podocyte protein structural anomalies. Other forms result from a totally different mechanism, which has not yet been elucidated. One of the proposed hypotheses suggests that cells from the immune system could produce one or several circulating factors, which would increase the glomerular permeability to proteins. In some cases, immunosuppressive drugs, in particular cyclosporin, can prove beneficial. However, the progression to end-stage renal failure is frequent. In this case, there is a risk of nephrotic syndrome recurrence after kidney transplant. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core
3308652010 A heterogeneous entity. Its prevalence in the general population is unknown. Nephrotic syndrome has manifestations of marked proteinuria, with reduced plasmatic levels of albumin, and potentially with edema. Familial forms are in most cases related to podocyte protein structural anomalies. Other forms result from a totally different mechanism, which has not yet been elucidated. One of the proposed hypotheses suggests that cells from the immune system could produce one or several circulating factors, which would increase the glomerular permeability to proteins. In some cases, immunosuppressive drugs, in particular cyclosporin, can prove beneficial. However, the progression to end-stage renal failure is frequent. In this case, there is a risk of nephrotic syndrome recurrence after kidney transplant. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core
3876121000052112 sporadiskt idiopatiskt steroidresistent nefrotiskt syndrom sv Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Sweden NRC maintained module (core metadata concept)

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Is a	Idiopathic disease	true	Inferred relationship	Some
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Is a	Steroid resistant nephrotic syndrome of childhood	true	Inferred relationship	Some
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Occurrence	Childhood	true	Inferred relationship	Some	4
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Finding site	Glomerulus structure	true	Inferred relationship	Some	3
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Has interpretation	Above reference range	true	Inferred relationship	Some	1
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Has interpretation	Below reference range	true	Inferred relationship	Some	2
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Interprets	Albumin measurement	true	Inferred relationship	Some	2
Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	Interprets	Measurement of protein in urine (procedure)	true	Inferred relationship	Some	1

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

This concept is not in any reference sets

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Id	Description	Lang	Type	Status	Case?	Module
3308645013	Sporadic idiopathic steroid-resistant nephrotic syndrome (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3308646014	Sporadic idiopathic steroid-resistant nephrotic syndrome	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3308647017	Sporadic idiopathic nephrosis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3308648010	A heterogeneous entity. Its prevalence in the general population is unknown. Nephrotic syndrome has manifestations of marked proteinuria, with reduced plasmatic levels of albumin, and potentially with oedema. Familial forms are in most cases related to podocyte protein structural anomalies. Other forms result from a totally different mechanism, which has not yet been elucidated. One of the proposed hypotheses suggests that cells from the immune system could produce one or several circulating factors, which would increase the glomerular permeability to proteins. In some cases, immunosuppressive drugs, in particular cyclosporin, can prove beneficial. However, the progression to end-stage renal failure is frequent. In this case, there is a risk of nephrotic syndrome recurrence after kidney transplant.	en	Definition	Inactive	Entire term case sensitive (core metadata concept)	SNOMED CT core
3308652010	A heterogeneous entity. Its prevalence in the general population is unknown. Nephrotic syndrome has manifestations of marked proteinuria, with reduced plasmatic levels of albumin, and potentially with edema. Familial forms are in most cases related to podocyte protein structural anomalies. Other forms result from a totally different mechanism, which has not yet been elucidated. One of the proposed hypotheses suggests that cells from the immune system could produce one or several circulating factors, which would increase the glomerular permeability to proteins. In some cases, immunosuppressive drugs, in particular cyclosporin, can prove beneficial. However, the progression to end-stage renal failure is frequent. In this case, there is a risk of nephrotic syndrome recurrence after kidney transplant.	en	Definition	Inactive	Entire term case sensitive (core metadata concept)	SNOMED CT core
3876121000052112	sporadiskt idiopatiskt steroidresistent nefrotiskt syndrom	sv	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Sweden NRC maintained module (core metadata concept)