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1228861004: Kaposiform lymphangiomatosis (disorder)

SNOMED CT Concept\Clinical finding\...

\Mass of body structure\Mass of soft tissue\Lymphangiomatosis\Kaposiform lymphangiomatosis

\General finding of soft tissue\Mass of soft tissue\Lymphangiomatosis\Kaposiform lymphangiomatosis
\General finding of soft tissue\Disorder of soft tissue\Soft tissue lesion\Lymphangiomatosis\Kaposiform lymphangiomatosis
\General finding of soft tissue\Disorder of soft tissue\Disorder of lymphatic vessel\Lymphatic malformation\Lymphangiomatosis\Kaposiform lymphangiomatosis

\Disease\Neoplasm and/or hamartoma\Angiomatosis\Lymphangiomatosis\Kaposiform lymphangiomatosis
\Disease\Disorder of body system\Disorder of lymphatic system\Disorder of lymphatic vessel\Lymphatic malformation\Lymphangiomatosis\Kaposiform lymphangiomatosis
\Disease\Congenital disease\Congenital anomaly\Lymphatic malformation\Lymphangiomatosis\Kaposiform lymphangiomatosis
\Disease\Disorder of soft tissue\Soft tissue lesion\Lymphangiomatosis\Kaposiform lymphangiomatosis
\Disease\Disorder of soft tissue\Disorder of lymphatic vessel\Lymphatic malformation\Lymphangiomatosis\Kaposiform lymphangiomatosis
\Disease\Developmental disorder\Congenital anomaly\Lymphatic malformation\Lymphangiomatosis\Kaposiform lymphangiomatosis

Status: current, Primitive. Date: 31-May 2022. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

5063491018 Kaposiform lymphangiomatosis (disorder) en Fully specified name Active Case insensitive SNOMED CT core

5063492013 Kaposiform lymphangiomatosis en Synonym Active Case insensitive SNOMED CT core

5063493015 A rare vascular anomaly or angioma with characteristics of multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnea, bleeding and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. en Definition Active Case sensitive SNOMED CT core

5063494014 A rare vascular anomaly or angioma with characteristics of multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnoea, bleeding and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. en Definition Active Case sensitive SNOMED CT core

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Kaposiform lymphangiomatosis	Is a	Lymphangiomatosis	true	Inferred relationship	Some
Kaposiform lymphangiomatosis	Occurrence	Congenital	true	Inferred relationship	Some	1
Kaposiform lymphangiomatosis	Finding site	Structure of lymphatic vessel	true	Inferred relationship	Some	1
Kaposiform lymphangiomatosis	Associated morphology	Lymphangiomatosis	true	Inferred relationship	Some	1
Kaposiform lymphangiomatosis	Pathological process	Pathological developmental process	true	Inferred relationship	Some	1

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

Reference Sets

Clinical finding foundation reference set

Neoplasm and/or hamartoma reference set

Problem/Diagnosis reference set

Back to Start

Id	Description	Lang	Type	Status	Case?	Module
5063491018	Kaposiform lymphangiomatosis (disorder)	en	Fully specified name	Active	Case insensitive	SNOMED CT core
5063492013	Kaposiform lymphangiomatosis	en	Synonym	Active	Case insensitive	SNOMED CT core
5063493015	A rare vascular anomaly or angioma with characteristics of multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnea, bleeding and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition.	en	Definition	Active	Case sensitive	SNOMED CT core
5063494014	A rare vascular anomaly or angioma with characteristics of multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnoea, bleeding and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition.	en	Definition	Active	Case sensitive	SNOMED CT core