1187508009: Immunoglobulin G4 related aortitis (disorder)

SNOMED CT Concept\Clinical finding\...

\Finding of trunk structure\Finding of aorta\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Finding of trunk structure\Disorder of trunk\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis

\General finding of soft tissue\Blood vessel finding\Arterial finding\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Blood vessel finding\Arterial finding\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Blood vessel finding\Arterial finding\Systemic arterial finding\Finding of aorta\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Blood vessel finding\Arterial finding\Systemic arterial finding\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Blood vessel finding\Vascular disorder\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Blood vessel finding\Vascular disorder\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Blood vessel finding\Vascular disorder\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Blood vessel finding\Vascular disorder\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis

\Cardiovascular finding\Cardiovascular disease\Inflammatory disorder of the cardiovascular system\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Cardiovascular disease\Inflammatory disorder of the cardiovascular system\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Cardiovascular disease\Vascular disorder\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Cardiovascular disease\Vascular disorder\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Cardiovascular disease\Vascular disorder\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Cardiovascular disease\Vascular disorder\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Arterial finding\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Arterial finding\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Arterial finding\Systemic arterial finding\Finding of aorta\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Arterial finding\Systemic arterial finding\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Vascular disorder\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Vascular disorder\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Vascular disorder\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Cardiovascular finding\Blood vessel finding\Vascular disorder\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis

\Disease\Disorder of immune function\Autoimmune disease\IgG4 related disease\Immunoglobulin G4 related aortitis
\Disease\Disorder of immune function\Autoimmune disease\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disorder of the cardiovascular system\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disorder of the cardiovascular system\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Cardiovascular disease\Inflammatory disorder of the cardiovascular system\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Cardiovascular disease\Inflammatory disorder of the cardiovascular system\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Cardiovascular disease\Vascular disorder\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Cardiovascular disease\Vascular disorder\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Cardiovascular disease\Vascular disorder\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of body system\Cardiovascular disease\Vascular disorder\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disorder of the cardiovascular system\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disorder of the cardiovascular system\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of trunk\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of soft tissue\Vascular disorder\Disorder of artery\Disease of non-coronary systemic artery\Disorder of aorta\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of soft tissue\Vascular disorder\Disorder of artery\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of soft tissue\Vascular disorder\Vasculitis\Autoimmune vasculitis\Immunoglobulin G4 related aortitis
\Disease\Disorder of soft tissue\Vascular disorder\Vasculitis\Arteritis\Vasculitis of large artery\Aortitis\Immunoglobulin G4 related aortitis

Status: current, Defined. Date: 31-Jan 2022. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

4674036013 Immunoglobulin G4 related aortitis (disorder) en Fully specified name Active Initial character case insensitive SNOMED CT core

4674037016 Immunoglobulin G4 related aortitis en Synonym Active Initial character case insensitive SNOMED CT core

4674038014 IgG4 (immunoglobulin G4) related aortitis en Synonym Active Case sensitive SNOMED CT core

4674040016 A rare systemic autoimmune disease with characteristics of infiltrates of IgG4 (immunoglobulin G4) positive plasma cells and lymphocytes in the adventitia of the aorta, resulting in thickening of perivascular tissue or formation of soft tissue masses surrounding the aorta and its major branches (potentially complicated by inflammatory aortic aneurysm), associated with elevated serum IgG4 levels. Preferential location is the infra-renal portion of the abdominal aorta. In addition, medium-sized blood vessels can be involved, and the condition may occur together with IgG4-related disease in other parts of the body. Clinical symptoms are unspecific and include chest or back pain and fever. en Definition Active Case sensitive SNOMED CT core

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Immunoglobulin G4 related aortitis	Is a	IgG4 related disease	true	Inferred relationship	Some
Immunoglobulin G4 related aortitis	Is a	Autoimmune vasculitis	true	Inferred relationship	Some
Immunoglobulin G4 related aortitis	Is a	Aortitis	true	Inferred relationship	Some
Immunoglobulin G4 related aortitis	Finding site	Aortic structure	true	Inferred relationship	Some	1
Immunoglobulin G4 related aortitis	Associated morphology	Inflammatory morphology	true	Inferred relationship	Some	1
Immunoglobulin G4 related aortitis	Pathological process	Autoimmune process	true	Inferred relationship	Some	1

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

Reference Sets

Clinical finding foundation reference set

Cardiovascular finding reference set

Problem/Diagnosis reference set

Back to Start

Id	Description	Lang	Type	Status	Case?	Module
4674036013	Immunoglobulin G4 related aortitis (disorder)	en	Fully specified name	Active	Initial character case insensitive	SNOMED CT core
4674037016	Immunoglobulin G4 related aortitis	en	Synonym	Active	Initial character case insensitive	SNOMED CT core
4674038014	IgG4 (immunoglobulin G4) related aortitis	en	Synonym	Active	Case sensitive	SNOMED CT core
4674040016	A rare systemic autoimmune disease with characteristics of infiltrates of IgG4 (immunoglobulin G4) positive plasma cells and lymphocytes in the adventitia of the aorta, resulting in thickening of perivascular tissue or formation of soft tissue masses surrounding the aorta and its major branches (potentially complicated by inflammatory aortic aneurysm), associated with elevated serum IgG4 levels. Preferential location is the infra-renal portion of the abdominal aorta. In addition, medium-sized blood vessels can be involved, and the condition may occur together with IgG4-related disease in other parts of the body. Clinical symptoms are unspecific and include chest or back pain and fever.	en	Definition	Active	Case sensitive	SNOMED CT core