Status: current, Defined. Date: 31-Jul 2021. Module: SNOMED CT core
Descriptions:
Id | Description | Lang | Type | Status | Case? | Module |
4574812012 | Dendritic cell sarcoma | en | Synonym | Active | Case insensitive | SNOMED CT core |
4574813019 | Dendritic cell sarcoma (disorder) | en | Fully specified name | Active | Case insensitive | SNOMED CT core |
4575711016 | Sarcoma of dendritic cells | en | Synonym | Active | Case insensitive | SNOMED CT core |
4574814013 | A rare dendritic cell tumour characterised by a neoplasm composed of spindled to ovoid cells with phenotypic features similar to those of normal indeterminate cells. The tumour cells consistently express S100 protein and CD1a, while langerin, specific B- and T-cell markers, CD30, the histiocytic marker CD163, and the follicular dendritic cell markers CD21, CD23, and CD35 are negative. Birbeck granules are absent on ultrastructural examination. Patients typically present with multiple papules, nodules, or plaques of the skin. Primary lymph node or splenic involvement is less common. Systemic symptoms are usually absent. The clinical course is highly variable. | en | Definition | Active | Case sensitive | SNOMED CT core |
4574815014 | A rare dendritic cell tumor characterized by a neoplasm composed of spindled to ovoid cells with phenotypic features similar to those of normal indeterminate cells. The tumor cells consistently express S100 protein and CD1a, while langerin, specific B- and T-cell markers, CD30, the histiocytic marker CD163, and the follicular dendritic cell markers CD21, CD23, and CD35 are negative. Birbeck granules are absent on ultrastructural examination. Patients typically present with multiple papules, nodules, or plaques of the skin. Primary lymph node or splenic involvement is less common. Systemic symptoms are usually absent. The clinical course is highly variable. | en | Definition | Active | Case sensitive | SNOMED CT core |
Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
Dendritic cell sarcoma | Is a | Primary malignant neoplasm | false | Inferred relationship | Some | ||
Dendritic cell sarcoma | Is a | Dendritic cell neoplasm | true | Inferred relationship | Some | ||
Dendritic cell sarcoma | Associated morphology | Dendritic cell sarcoma | true | Inferred relationship | Some | 1 | |
Dendritic cell sarcoma | Is a | Malignant histiocytic disorder | true | Inferred relationship | Some | ||
Dendritic cell sarcoma | Is a | Sarcoma | true | Inferred relationship | Some |
Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
Reference Sets
Australian emergency department reference set
Clinical finding foundation reference set
Neoplasm and/or hamartoma reference set
Problem/Diagnosis reference set