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773691007: dermatose érosive et vésiculaire congénitale (trouble)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3725796017 Congenital erosive and vesicular dermatosis with reticulated supple scarring en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725797014 Congenital erosive and vesicular dermatosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725798016 CEVD - congenital erosive and vesicular dermatosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3725799012 Congenital erosive and vesicular dermatosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
771881000241116 dermatose érosive et vésiculaire congénitale (trouble) fr Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT Common French translation module (core metadata concept)
953831000172115 dermatose érosive et vésiculeuse congénitale avec cicatrices réticulées fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Common French translation module (core metadata concept)
994411000172119 dermatose érosive et vésiculaire congénitale fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Common French translation module (core metadata concept)
3725800011 A rare idiopathic skin disease with characteristics of widespread, congenital, superficial erosions and vesicles (often involving more than 75% of the body) which heal leaving scars with a supple, symmetrical, reticulated pattern, frequently resulting in cicatricial alopecia and hyperthermia and/or hypohidrosis. Nail anomalies, neurodevelopmental and ophthalmologic abnormalities, tongue atrophy and preterm birth, with or without history of chorioamnionitis, are commonly associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Congenital erosive and vesicular dermatosis est un(e) (attribut) maladie idiopathique true Inferred relationship Some
Congenital erosive and vesicular dermatosis survenue (attribut) congénital true Inferred relationship Some 1
Congenital erosive and vesicular dermatosis Pathological process (attribute) Pathological developmental process true Inferred relationship Some 1
Congenital erosive and vesicular dermatosis survenue (attribut) congénital true Inferred relationship Some 2
Congenital erosive and vesicular dermatosis morphologie associée (attribut) Vesicular inflammation true Inferred relationship Some 2
Congenital erosive and vesicular dermatosis est un(e) (attribut) ulcère cutané true Inferred relationship Some
Congenital erosive and vesicular dermatosis Pathological process (attribute) Pathological developmental process true Inferred relationship Some 2
Congenital erosive and vesicular dermatosis morphologie associée (attribut) Ulcerative inflammation true Inferred relationship Some 1
Congenital erosive and vesicular dermatosis est un(e) (attribut) Congenital anomaly of skin true Inferred relationship Some
Congenital erosive and vesicular dermatosis localisation d'une constatation (attribut) structure de la peau true Inferred relationship Some 2
Congenital erosive and vesicular dermatosis est un(e) (attribut) Inflammatory dermatosis (disorder) true Inferred relationship Some
Congenital erosive and vesicular dermatosis localisation d'une constatation (attribut) structure de la peau true Inferred relationship Some 1
Congenital erosive and vesicular dermatosis est un(e) (attribut) inflammation d'un organe corporel spécifique false Inferred relationship Some
Congenital erosive and vesicular dermatosis est un(e) (attribut) Vesicle of skin (finding) true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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