Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-May 2022. Module: SNOMED CT core
Descriptions:
| Id | Description | Lang | Type | Status | Case? | Module |
| 5063491018 | Kaposiform lymphangiomatosis (disorder) | en | Fully specified name | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
| 5063492013 | Kaposiform lymphangiomatosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
| 5063493015 | A rare vascular anomaly or angioma with characteristics of multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnea, bleeding and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| 5063494014 | A rare vascular anomaly or angioma with characteristics of multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnoea, bleeding and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
| Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
| Kaposiform lymphangiomatosis (disorder) | Is a | Lymphangiomatosis (disorder) | true | Inferred relationship | Some | ||
| Kaposiform lymphangiomatosis (disorder) | Occurrence | Congenital | true | Inferred relationship | Some | 1 | |
| Kaposiform lymphangiomatosis (disorder) | Finding site | Structure of lymphatic vessel | true | Inferred relationship | Some | 1 | |
| Kaposiform lymphangiomatosis (disorder) | Associated morphology | Lymphangiomatosis | true | Inferred relationship | Some | 1 | |
| Kaposiform lymphangiomatosis (disorder) | Pathological process (attribute) | Pathological developmental process | true | Inferred relationship | Some | 1 |
| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
This concept is not in any reference sets
FHIR