773688007: Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

SNOMED CT Concept\Clinical finding (finding)\...

\Finding of back (finding)\Finding of spinal region\Disorder of spinal region (disorder)\Spinal cord disorder (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Finding of back (finding)\Finding of spinal region\Disorder of spinal region (disorder)\Spinal cord disorder (disorder)\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Finding of back (finding)\Finding of spinal region\Finding of spinal cord\Spinal cord disorder (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Finding of back (finding)\Finding of spinal region\Finding of spinal cord\Spinal cord disorder (disorder)\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Finding of back (finding)\Disorder of back\Disorder of spinal region (disorder)\Spinal cord disorder (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Finding of back (finding)\Disorder of back\Disorder of spinal region (disorder)\Spinal cord disorder (disorder)\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

\Central nervous system finding\Finding of spinal cord\Spinal cord disorder (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Finding of spinal cord\Spinal cord disorder (disorder)\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Finding of brain\Disorder of brain (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Finding of brain\Disorder of brain (disorder)\Disorder of brain stem (disorder)\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Finding of brain\Disorder of brain (disorder)\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Finding of brain\Disorder of brain (disorder)\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Disorder of brain stem (disorder)\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Spinal cord disorder (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Spinal cord disorder (disorder)\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Inflammatory disease of the central nervous system\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Inflammatory disease of the central nervous system\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Central nervous system finding\Disorder of the central nervous system (disorder)\Inflammatory disease of the central nervous system\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

\Finding of head and neck region\Head finding (finding)\...

\Finding of brain\Disorder of brain (disorder)\...

\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

\Disorder of brain stem (disorder)\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

\Disorder of head (disorder)\Inflammatory disorder of head\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disorder of head (disorder)\Inflammatory disorder of head\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disorder of head (disorder)\Disorder of brain (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disorder of head (disorder)\Disorder of brain (disorder)\Disorder of brain stem (disorder)\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disorder of head (disorder)\Disorder of brain (disorder)\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disorder of head (disorder)\Disorder of brain (disorder)\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

\Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disease of the central nervous system\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disease of the central nervous system\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disease of the central nervous system\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Disorder of brain stem (disorder)\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Disorder of brain (disorder)\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Spinal cord disorder (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Spinal cord disorder (disorder)\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Inflammatory disease of the central nervous system\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Inflammatory disease of the central nervous system\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of body system\Disorder of nervous system (disorder)\Disorder of the central nervous system (disorder)\Inflammatory disease of the central nervous system\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammatory disorder of head\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammatory disorder of head\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disease of the central nervous system\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disease of the central nervous system\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disease of the central nervous system\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of head (disorder)\Inflammatory disorder of head\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of head (disorder)\Inflammatory disorder of head\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of head (disorder)\Disorder of brain (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of head (disorder)\Disorder of brain (disorder)\Disorder of brain stem (disorder)\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of head (disorder)\Disorder of brain (disorder)\Encephalitis\Brainstem encephalitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of head (disorder)\Disorder of brain (disorder)\Encephalitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of back\Disorder of spinal region (disorder)\Spinal cord disorder (disorder)\Encephalomyelopathy (disorder)\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)
\Disease\Disorder of back\Disorder of spinal region (disorder)\Spinal cord disorder (disorder)\Myelitis\Encephalomyelitis\Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

3725773017 CLIPPERS - chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core

3725774011 Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core

3725775012 Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

3725778014 A rare neuroinflammatory disorder with characteristics of brainstem-predominant encephalomyelitis, which typically presents with cerebellar and cranial nerve manifestations (gait ataxia, dysarthria, visual disorders, parasthesia), as well as brainstem, myelopathy and cognitive findings that respond to steroid treatment. Punctate curvilinear post-gadolinium contrast enhancement predominantly in the pons and cerebellum is observed on brain MRI and prominent, perivascular, CD3+ T-cell predominantly lymphocytic inflammation in neuropathology. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

10055851000172111 inflammation lymphocytaire chronique avec rehaussement périvasculaire pontique corticosensible fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) Belgian module (core metadata concept)

10055861000172113 syndrome de CLIPPERS (chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids) fr Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) Belgian module (core metadata concept)

4886611000172114 CLIPPERS nl Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) Belgian module (core metadata concept)

4886621000172116 chronische lymfocytaire ontsteking met pontiene perivasculaire verbetering reagerend op steroïden nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) Belgian module (core metadata concept)

4886631000172118 chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) Belgian module (core metadata concept)

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)	Is a	Brainstem encephalitis	true	Inferred relationship	Some
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)	Is a	Encephalomyelitis	true	Inferred relationship	Some
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)	Associated morphology	Chronic lymphocytic inflammation	true	Inferred relationship	Some	2
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)	Finding site	Brainstem structure	true	Inferred relationship	Some	2
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)	Finding site	Spinal cord structure	true	Inferred relationship	Some	1
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)	Associated morphology	Chronic lymphocytic inflammation	true	Inferred relationship	Some	1

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

Reference Sets

Belgian subset for medical problems in patient health records

Back to Start

Id	Description	Lang	Type	Status	Case?	Module
3725773017	CLIPPERS - chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids	en	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
3725774011	Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3725775012	Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3725778014	A rare neuroinflammatory disorder with characteristics of brainstem-predominant encephalomyelitis, which typically presents with cerebellar and cranial nerve manifestations (gait ataxia, dysarthria, visual disorders, parasthesia), as well as brainstem, myelopathy and cognitive findings that respond to steroid treatment. Punctate curvilinear post-gadolinium contrast enhancement predominantly in the pons and cerebellum is observed on brain MRI and prominent, perivascular, CD3+ T-cell predominantly lymphocytic inflammation in neuropathology.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
10055851000172111	inflammation lymphocytaire chronique avec rehaussement périvasculaire pontique corticosensible	fr	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	Belgian module (core metadata concept)
10055861000172113	syndrome de CLIPPERS (chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids)	fr	Synonym (core metadata concept)	Active	Only initial character case insensitive (core metadata concept)	Belgian module (core metadata concept)
4886611000172114	CLIPPERS	nl	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	Belgian module (core metadata concept)
4886621000172116	chronische lymfocytaire ontsteking met pontiene perivasculaire verbetering reagerend op steroïden	nl	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	Belgian module (core metadata concept)
4886631000172118	chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids	nl	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	Belgian module (core metadata concept)