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761958009: maligne perineurioom (aandoening)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2018. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3634392015 Malignant peripheral nerve sheath tumour with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634393013 Malignant peripheral nerve sheath neoplasm with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634394019 Malignant peripheral nerve sheath tumor with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634395018 Malignant peripheral nerve sheath neoplasm with perineurial differentiation (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634396017 Malignant perineurioma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3954641000146113 maligne perineurioom (aandoening) nl Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
3954651000146111 maligne perineurioom nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
3954661000146114 perineurale MPNST nl Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
3634399012 A rare soft tissue sarcoma composed predominantly of spindle-shaped neoplastic cells showing perineurial differentiation and displaying abundant cellular pleomorphism or anaplasia, frequent mitoses, tumour necrosis and high metastatic potential. It often presents as a soft, painless, solid mass in subcutaneous tissues of the trunk or limbs, but tumours have also been described in the facial area, mediastinum, retroperitoneum, pancreas, paravertebral column and the pelvic soft tissues. Frequent local recurrence and distant metastatic spread has been reported. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core
3634400017 A rare soft tissue sarcoma composed predominantly of spindle-shaped neoplastic cells showing perineurial differentiation and displaying abundant cellular pleomorphism or anaplasia, frequent mitoses, tumor necrosis and high metastatic potential. It often presents as a soft, painless, solid mass in subcutaneous tissues of the trunk or limbs, but tumors have also been described in the facial area, mediastinum, retroperitoneum, pancreas, paravertebral column and the pelvic soft tissues. Frequent local recurrence and distant metastatic spread has been reported. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core


1 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Malignant peripheral nerve sheath tumour with perineurial differentiation Associated morphology Perineurioma, malignant true Inferred relationship Some 1
Malignant peripheral nerve sheath tumour with perineurial differentiation Is a Malignant peripheral nerve sheath tumor (disorder) true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group
Primary malignant peripheral nerve sheath tumour with perineurial differentiation Is a True Malignant peripheral nerve sheath tumour with perineurial differentiation Inferred relationship Some

This concept is not in any reference sets

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