718096004: hepatoportale sclerose (aandoening)

SNOMED CT Concept\Clinical finding (finding)\...

\Finding of trunk structure\Finding of abdominopelvic segment of trunk (finding)\Disorder of abdominopelvic segment of trunk\Disorder of abdomen (disorder)\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Finding of trunk structure\Finding of abdominopelvic segment of trunk (finding)\Finding of abdomen\Disorder of abdomen (disorder)\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of abdominopelvic segment of trunk\Disorder of abdomen (disorder)\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of soft tissue of trunk\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)

\General finding of soft tissue\Blood vessel finding\Venous finding\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\General finding of soft tissue\Blood vessel finding\Vascular disorder\Vascular degeneration\Hepatoportal sclerosis (disorder)
\General finding of soft tissue\Blood vessel finding\Vascular disorder\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\General finding of soft tissue\Blood vessel finding\Vascular disorder\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Disorder of soft tissue of trunk\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Vascular degeneration\Hepatoportal sclerosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)

\Cardiovascular finding\Disorder of cardiovascular system (disorder)\Vascular disorder\Vascular degeneration\Hepatoportal sclerosis (disorder)
\Cardiovascular finding\Disorder of cardiovascular system (disorder)\Vascular disorder\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Cardiovascular finding\Disorder of cardiovascular system (disorder)\Vascular disorder\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Cardiovascular finding\Blood vessel finding\Venous finding\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Cardiovascular finding\Blood vessel finding\Vascular disorder\Vascular degeneration\Hepatoportal sclerosis (disorder)
\Cardiovascular finding\Blood vessel finding\Vascular disorder\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Cardiovascular finding\Blood vessel finding\Vascular disorder\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)

\Disease\Degenerative disorder\Vascular degeneration\Hepatoportal sclerosis (disorder)
\Disease\Disorder of body system\Disorder of cardiovascular system (disorder)\Vascular disorder\Vascular degeneration\Hepatoportal sclerosis (disorder)
\Disease\Disorder of body system\Disorder of cardiovascular system (disorder)\Vascular disorder\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Disease\Disorder of body system\Disorder of cardiovascular system (disorder)\Vascular disorder\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of abdominopelvic segment of trunk\Disorder of abdomen (disorder)\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of soft tissue of trunk\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Disease\Disorder of soft tissue\Disorder of soft tissue of trunk\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Disease\Disorder of soft tissue\Vascular disorder\Vascular degeneration\Hepatoportal sclerosis (disorder)
\Disease\Disorder of soft tissue\Vascular disorder\Vascular disease of abdomen (disorder)\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)
\Disease\Disorder of soft tissue\Vascular disorder\Disorder of vein\Disorder of portal venous system\Disorder of hepatic portal vein\Hepatoportal sclerosis (disorder)

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2016. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

3311104019 Hepatoportal sclerosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core

3311147019 Hepatoportal sclerosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

3311148012 Obliterative portal venopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

7099711000146110 hepatoportale sclerose nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)

7099721000146117 hepatoportale sclerose (aandoening) nl Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)

3311149016 A rare disorder with characteristics of sclerosis of the intrahepatic portal veins, non-cirrhotic portal hypertension, asymptomatic splenomegaly and recurrent variceal bleeding. Most commonly, the condition is detected in investigating a fortuitous finding of hypersplenism or splenomegaly. Main histopathologic findings are periportal fibrosis, occlusion of small portal veins, sclerosis of the portal venous system, and proliferation of small vascular channels within/around portal tracts. The disease is slowly progressive. Exposure to toxic substances or drugs, autoimmune and connective tissue diseases, systemic or intraabdominal infections, and clotting abnormalities have been incriminated. A genetic background has been suggested. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Hepatoportal sclerosis (disorder)	Is a	Disorder of hepatic portal vein	true	Inferred relationship	Some
Hepatoportal sclerosis (disorder)	Is a	Degenerative disorder	false	Inferred relationship	Some
Hepatoportal sclerosis (disorder)	Associated morphology	Vascular sclerosis	true	Inferred relationship	Some	1
Hepatoportal sclerosis (disorder)	Finding site	Structure of intrahepatic part of main portal vein (body structure)	true	Inferred relationship	Some	1
Hepatoportal sclerosis (disorder)	Is a	Vascular degeneration	true	Inferred relationship	Some

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

Reference Sets

Description inactivation indicator reference set

Back to Start

Id	Description	Lang	Type	Status	Case?	Module
3311104019	Hepatoportal sclerosis (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3311147019	Hepatoportal sclerosis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
3311148012	Obliterative portal venopathy	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
7099711000146110	hepatoportale sclerose	nl	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Netherlands NRC maintained module (core metadata concept)
7099721000146117	hepatoportale sclerose (aandoening)	nl	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Netherlands NRC maintained module (core metadata concept)
3311149016	A rare disorder with characteristics of sclerosis of the intrahepatic portal veins, non-cirrhotic portal hypertension, asymptomatic splenomegaly and recurrent variceal bleeding. Most commonly, the condition is detected in investigating a fortuitous finding of hypersplenism or splenomegaly. Main histopathologic findings are periportal fibrosis, occlusion of small portal veins, sclerosis of the portal venous system, and proliferation of small vascular channels within/around portal tracts. The disease is slowly progressive. Exposure to toxic substances or drugs, autoimmune and connective tissue diseases, systemic or intraabdominal infections, and clotting abnormalities have been incriminated. A genetic background has been suggested.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core