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1963002: paroxismale nachtelijke hemoglobinurie (aandoening)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
4387014 Paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4388016 Marchiafava-Micheli syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
479750016 Paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
747959018 Paroxysmal nocturnal hemoglobinuria (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5244076012 PNH - paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5244077015 PNH - paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
336981000146115 syndroom van Marchiafava-Micheli nl Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
11181601000146111 paroxismale nachtelijke hemoglobinurie nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
11181611000146113 paroxismale nachtelijke hemoglobinurie (aandoening) nl Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
13079881000146110 PNH; bloedarmoede door een versterkte in aanvallen optredende afbraak van rode bloedcellen. nl Definition Active Entire term case sensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Paroxysmal nocturnal haemoglobinuria Is a Anaemia due to intrinsic red cell abnormality true Inferred relationship Some
Paroxysmal nocturnal haemoglobinuria Finding site Erythrocyte false Inferred relationship Some
Paroxysmal nocturnal haemoglobinuria Finding site Hematopoietic system structure false Inferred relationship Some
Paroxysmal nocturnal haemoglobinuria Onset Sudden false Inferred relationship Some
Paroxysmal nocturnal haemoglobinuria Onset Sudden onset false Inferred relationship Some
Paroxysmal nocturnal haemoglobinuria Has definitional manifestation erytropenie (bevinding) false Inferred relationship Some
Paroxysmal nocturnal haemoglobinuria Finding site Hematopoietic system structure false Inferred relationship Some
Paroxysmal nocturnal haemoglobinuria Has interpretation Below reference range false Inferred relationship Some 1
Paroxysmal nocturnal haemoglobinuria Interprets Measurement of total haemoglobin concentration false Inferred relationship Some 1
Paroxysmal nocturnal haemoglobinuria Has interpretation Below reference range false Inferred relationship Some 2
Paroxysmal nocturnal haemoglobinuria Interprets Red blood cell count false Inferred relationship Some 2

Inbound Relationships Type Active Source Characteristic Refinability Group
Thrombophilia due to paroxysmal nocturnal haemoglobinuria Due to True Paroxysmal nocturnal haemoglobinuria Inferred relationship Some 1
Occlusion of microvasculature of skin due to paroxysmal nocturnal hemoglobinuria-associated platelet plugs (disorder) Due to True Paroxysmal nocturnal haemoglobinuria Inferred relationship Some 2

Reference Sets

Dutch pathology simple reference set (foundation metadata concept)

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