1156801007: macrofaagactivatiesyndroom door systemische juveniele idiopathische artritis (aandoening)

SNOMED CT Concept\Clinical finding (finding)\...

\Temperature-associated finding\Body temperature finding\Abnormal body temperature\Body temperature above reference range\Febrile disorder (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis

\Finding of blood, lymphatics and immune system\Disorder of cellular component of blood (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\...

\Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis

\Macrophage activation syndrome (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis

\Vital signs finding\Body temperature finding\Abnormal body temperature\Body temperature above reference range\Febrile disorder (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis

\Disease\Febrile disorder (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of immune function (disorder)\Immunodeficiency disorder\Primary immune deficiency disorder\Phagocytic cell defect\Phagocytic cell dysfunction\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of immune function (disorder)\Immunodeficiency disorder\Primary immune deficiency disorder\Phagocytic cell defect\Phagocytic cell dysfunction\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Macrophage activation syndrome (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of immune function (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of immune function (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Macrophage activation syndrome (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of hematopoietic cell proliferation (disorder)\Histiocytic syndrome\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of hematopoietic cell proliferation (disorder)\Histiocytic syndrome\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Macrophage activation syndrome (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of cellular component of blood (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of cellular component of blood (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Macrophage activation syndrome (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of body system\Hematological disorder (disorder)\Disorder of hematopoietic structure (disorder)\Haemophagocytic lymphohistiocytosis\Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of body system\Hematological disorder (disorder)\Disorder of hematopoietic structure (disorder)\Haemophagocytic lymphohistiocytosis\Macrophage activation syndrome (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of body system\Disorder of immune structure (disorder)\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis
\Disease\Disorder of body system\Disorder of immune structure (disorder)\Combined phagocytic defect\Hemolytic erythrophagocytic syndrome\Haemophagocytic lymphohistiocytosis\Macrophage activation syndrome (disorder)\Macrophage activation syndrome due to juvenile systemic onset arthritis

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2021. Module: SNOMED CT core

Descriptions:

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Macrophage activation syndrome due to juvenile systemic onset arthritis	Associated with	Autoimmune disease	false	Inferred relationship	Some	4
Macrophage activation syndrome due to juvenile systemic onset arthritis	Associated morphology	histiocytose - categorie (afwijkende morfologie)	false	Inferred relationship	Some	3
Macrophage activation syndrome due to juvenile systemic onset arthritis	Pathological process (attribute)	Abnormal immune process (qualifier value)	false	Inferred relationship	Some	3
Macrophage activation syndrome due to juvenile systemic onset arthritis	Finding site	Mononuclear phagocyte system structure (body structure)	false	Inferred relationship	Some	3
Macrophage activation syndrome due to juvenile systemic onset arthritis	Is a	Macrophage activation syndrome (disorder)	true	Inferred relationship	Some
Macrophage activation syndrome due to juvenile systemic onset arthritis	Due to	Systemic onset juvenile chronic arthritis (disorder)	true	Inferred relationship	Some	2
Macrophage activation syndrome due to juvenile systemic onset arthritis	Is a	Febrile disorder (disorder)	true	Inferred relationship	Some
Macrophage activation syndrome due to juvenile systemic onset arthritis	Finding site	Mononuclear phagocyte system structure (body structure)	true	Inferred relationship	Some	1
Macrophage activation syndrome due to juvenile systemic onset arthritis	Associated morphology	Histiocytic proliferation (morphologic abnormality)	true	Inferred relationship	Some	1
Macrophage activation syndrome due to juvenile systemic onset arthritis	Pathological process (attribute)	Abnormal immune process (qualifier value)	true	Inferred relationship	Some	1
Macrophage activation syndrome due to juvenile systemic onset arthritis	Interprets	Body temperature (observable entity)	true	Inferred relationship	Some	3
Macrophage activation syndrome due to juvenile systemic onset arthritis	Has interpretation	Above reference range	true	Inferred relationship	Some	3
Macrophage activation syndrome due to juvenile systemic onset arthritis	Is a	Hemophagocytic lymphohistiocytosis due to systemic disease (disorder)	true	Inferred relationship	Some

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

This concept is not in any reference sets

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Id	Description	Lang	Type	Status	Case?	Module
4577614016	Macrophage activation syndrome due to juvenile systemic onset arthritis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
4577615015	Macrophage activation syndrome due to juvenile systemic onset arthritis (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
12953611000146117	macrofaagactivatiesyndroom door systemische juveniele idiopathische artritis (aandoening)	nl	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Netherlands NRC maintained module (core metadata concept)
12953621000146110	macrofaagactivatiesyndroom door systemische juveniele idiopathische artritis	nl	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Netherlands NRC maintained module (core metadata concept)
12953631000146112	macrofaagactivatiesyndroom door ziekte van Still	nl	Synonym (core metadata concept)	Active	Only initial character case insensitive (core metadata concept)	SNOMED CT Netherlands NRC maintained module (core metadata concept)